The rare autosomal recessive form of the vascular type of Ehlers-Danlos syndrome. vEDS is almost always inherited in an autosomal dominant manner but rare examples of biallelic inheritance have been reported. The disease is autosomal recessive Ehlers-Danlos syndrome, vascular type (MONDO_0002014, a Monarch Disease Ontology term). Also known as: Ehlers-Danlos syndrome, recessive type 4, Ehlers-Danlos syndrome, vascular type, autosomal recessive, autosomal recessive type IV Ehlers-Danlos syndrome.