Familial embryonal neoplasm derived from nephrogenic blastemal cells. Several lines of differentiation, including blastemal, stromal and epithelial, are usually expressed. Comprises approximately 1% of Wilms tumors. (AFIP fascicle version 2.0). The disease is Monarch Disease Ontology id MONDO_0003321 (hereditary Wilms tumor). Also known as: familial Wilms tumor, familial Wilms tumour, familial Wilms' tumor, familial Wilms' tumour, hereditary Wilms' tumor, hereditary Wilms' tumour, hereditary kidney adenosarcoma, hereditary nephroblastoma.