MONDO_0006190 (endolymphatic sac tumor) is an aggressive epithelial neoplasm arising from the temporal bone. It is characterized by the presence of a papillary pattern, and has been described as an adenoma or carcinoma in the literature. There is disagreement regarding its relationship to endolymphatic sac tumor. Also known as: ELST, aggressive papillary tumor of the temporal bone, aggressive papillary tumour of the temporal bone, endolymphatic sac neoplasm, endolymphatic sac neoplasm (disease), endolymphatic sac tumor (disease), endolymphatic sac tumour (disease), neoplasm of endolymphatic sac.