lung lymphangioleiomyomatosis (MONDO_0006277, a Monarch Disease Ontology term) is lymphangiomyomatosis involving the lungs and local lymph nodes. Patients usually present with chylous pleural effusion. The clinical course is variable. Patients with resectable lesions usually have a favorable clinical outcome. Patients with diffuse lesions usually have a progressive clinical course. Also known as: lung lymphangiomyomatosis, pulmonary lymphangioleiomyomatosis.