An aggressive, progressive, and destructive lesion affecting the nasal cavities, paranasal sinuses, and the palate. The vast majority of cases are malignant lymphoproliferations affecting the midline of the face in patients with nasal type extranodal NK/T-cell lymphoma. The disease is nasal cavity and paranasal sinus lethal midline granuloma (MONDO_0006828). Also known as: Midline lethal granuloma of nasal cavity and paranasal sinus, Midline lethal granuloma of the nasal cavity and paranasal sinus, malignant granuloma of face, midfacial Necrotising lesion, nasal cavity and paranasal sinus lethal Midline granuloma.