Monarch Disease Ontology id MONDO_0007273 (pheochromocytoma/paraganglioma syndrome 4) is an autosomal dominant tumor predisposition disorder caused by pathogenic variants in the SDHB gene, characterized by an increased risk of paraganglioma and pheochromocytoma, as well as an increased risk of renal cell carcinoma and gastrointestinal stromal tumors (GIST). Also known as: SDHB paraganglioma, SDHB-related tumor predisposition, paraganglioma caused by mutation in SDHB, paragangliomas 4, paragangliomas type 4.