Inherited or familial Creutzfeldt-Jakob disease (fCJD) is a very rare form of genetic prion disease characterized by typical CJD features (rapidly progressive dementia, personality/behavioral changes, psychiatric disorders, myoclonus, and ataxia) with a genetic cause and sometimes a family history of dementia. The disease is MONDO_0007403 (inherited Creutzfeldt-Jakob disease). Also known as: Creutzfeldt-Jakob disease, variant, resistance to, hereditary Creutzfeldt Jacob disease, inherited CJD.