Benign concentric annular macular dystrophy (BCAMD) is a progressive autosomal dominant macular dystrophy characterized by parafoveal hypopigmentation followed by a retinitis pigmentosa-like phenotype (nyctalopia and peripheral vision loss) with a bullBs eye configuration. The disease is benign concentric annular macular dystrophy (MONDO_0007934, a Monarch Disease Ontology term). Also known as: retinitis pigmentosa 91.