MONDO_0008073 (familial juvenile hyperuricemic nephropathy type 1) is a rare kidney disorder characterized by hyperuricemia, progressive nephropathy, and gout occurring at an early age. Also known as: ADTKD-UMOD, Autosomal Dominant Tubulo-Interstitial Kidney Disease, FJHN type 1, HNFJ1, UMOD familial juvenile hyperuricemic nephropathy, UMOD-associated FJHN, UMOD-associated familial juvenile hyperuricemic nephropathy, UMOD-related ADTKD.