Kindler syndrome (KS) is the fourth major type of epidermolysis bullosa (EB), besides simplex, junctional and dystrophic forms, and is characterized by skin fragility and blistering at birth followed by development of photosensitivity and progressive poikilodermatous skin changes. The disease is Kindler syndrome (MONDO_0008260, a Monarch Disease Ontology id). Also known as: KS, poikiloderma of Kindler.