Ring dermoid of cornea is characterized by annular limbal dermoids (growths with a skin-like structure) with corneal and conjunctival extension. Less than 30 cases have been described. Transmission is autosomal dominant and mutations in the PITX2 gene have been suggested as a potential cause of the condition. The disease is Monarch Disease Ontology id MONDO_0008387 (ring dermoid of cornea). Also known as: Ring dermoid syndrome.