Monarch Disease Ontology entry MONDO_0008681 (WAGR syndrome) (Wilms tumor - aniridia - genitourinary anomalies - intellectual disability mental retardation) is a rare genetic disorder characterized by an unusual complex of congenital developmental abnormalities with intellectual disability, and an increased risk of developing Wilms tumor. Also known as: 11p partial monosomy syndrome, Del(11)(p13), WAGR 11p13 deletion syndrome, WAGR Syndrome/11p Deletion Syndrome, Wilms tumor, aniridia, genitourinary anomalies and developmental delay syndrome, Wilms tumor, aniridia, genitourinary anomalies and mental retardation syndrome, autosomal dominant, somatic mutation, Wilms tumor-aniridia-genitourinary anomalies-intellectual disability syndrome, Wilms tumor-aniridia-genitourinary anomalies-mental retardation syndrome.