MONDO_0008682 (Denys-Drash syndrome) (DDS) is a rare urogenital disorder characterized by the association of diffuse mesangial sclerosis (DMS), male pseudohermaphroditism with a 46,XY karyotype, and nephroblastoma. Also known as: Denys Drash syndrome, Denys-Drash syndrome, autosomal dominant, somatic mutation, Drash syndrome, Wilms tumor and pseudohermaphroditism, Wilms tumour and pseudohermaphroditism, nephrotic syndrome type 4.