Congenital lipoid adrenal hyperplasia (CLAH) is one of the most severe forms of congenital adrenal hyperplasia (CAH) characterized by severe adrenal insufficiency and sex reversal in males. The disease is Monarch Disease Ontology term MONDO_0008725 (congenital lipoid adrenal hyperplasia due to STAR deficency). Also known as: CLAH, lipoid adrenal hyperplasia.