Monarch Disease Ontology term MONDO_0009281 (glutaryl-CoA dehydrogenase deficiency) can be described as follows. Glutaryl-CoA dehydrogenase (GCDH) deficiency (GDD) is an autosomal recessive neurometabolic disorder clinically characterized by encephalopathic crises resulting in striatal injury and a severe dystonic dyskinetic movement disorder. Also known as: GA1, GCDHD, glutaric acidemia type 1, glutaric aciduria type 1, glutaric aciduria, type 1, glutaricaciduria, type I, glutaryl-coenzyme A dehydrogenase deficiency.