Hepatic veno-occlusive disease-immunodeficiency syndrome is characterized by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centers, absent tissue plasma cells and hepatic veno-occlusive disease. The disease is hepatic veno-occlusive disease-immunodeficiency syndrome (MONDO_0009338). Also known as: VODI syndrome.