Mucopolysaccharidosis type 6 (MPS 6) is a lysosomal storage disease with progressive multisystem involvement, associated with a deficiency of arylsulfatase B (ASB) leading to the accumulation of dermatan sulfate. The disease is mucopolysaccharidosis type 6 (MONDO_0009661, a Monarch Disease Ontology term). Also known as: ARSB deficiency, ASB deficiency, MPS VI - Maroteaux-Lamy syndrome, MPS6, MPSVI, Maroteaux - Lamy syndrome, Maroteaux Lamy Syndrome, Maroteaux-Lamy disease.