3-methylglutaconic aciduria type 3 (MONDO_0009787) can be described as follows. 3-methylglutaconic aciduria type III (MGA III) is an organic aciduria characterized by the association of optic atrophy and choreoathetosis with 3-methylglutaconic aciduria. Also known as: 3-methylglutaconic aciduria caused by mutation in OPA3, 3-methylglutaconic aciduria type III, Costeff optic atrophy syndrome, Costeff syndrome, Iraqi-Jewish optic atrophy plus, MGA3, OPA3 3-methylglutaconic aciduria, autosomal recessive optic atrophy plus syndrome.