Congenital pulmonary lymphangiectasia (PL) is a rare developmental disorder involving the lung and characterized by pulmonary subpleural, interlobar, perivascular, and peribronchial lymphatic dilatation. The disease is Monarch Disease Ontology id MONDO_0009933 (congenital pulmonary lymphangiectasia). Also known as: Diffuse Pulmonary Lymphangiomatosis, congenital pulmonary lymphangiectasis, pulmonary lymphangiomatosis.