Monarch Disease Ontology id MONDO_0010171 (Usher syndrome type 1C) can be described as follows. A form of Usher syndrome type I that is caused by homozygous or compound heterozygous mutation in the gene encoding harmonin on chromosome 11p15. It is inherited in an autosomal recessive manner. Also known as: USH1C, Usher syndrome type I Acadian variety, Usher syndrome type IC.