Monarch Disease Ontology identifier MONDO_0010246 (developmental and epileptic encephalopathy, 9) can be described as follows. Female restricted epilepsy with intellectual disability is a rare X-linked epilepsy syndrome characterized by febrile or afebrile seizures (mainly tonic-clonic, but also absence, myoclonic, and atonic) starting in the first years of life and, in most cases, developmental delay and intellectual disability of variable severity. Behavioral disturbances (e.g. autistic features, hyperactivity, and aggressiveness) are also frequently associated. This disease affects exclusively females, with male carriers being unaffected, despite an X-linked inheritance. Also known as: DEE9, EFMR, EIEE9, Juberg Hellman syndrome, Juberg-Hellman syndrome, PCDH19 early infantile epileptic encephalopathy, developmental and epileptic encephalopathy 9, early infantile epileptic encephalopathy 9.