Dent disease type 2 is a type of Dent disease in which patients have the manifestations of Dent disease type 1 associated with extra-renal features. The disease is Dent disease type 2 (Monarch Disease Ontology identifier MONDO_0010359). Also known as: Dent disease caused by mutation in OCRL, OCRL Dent disease, dent disease 2, X-linked recessive, nephrolithiasis type 2.