Monarch Disease Ontology term MONDO_0010750 (ulnar hypoplasia-split foot syndrome) is characterized by the association of severe ulnar hypoplasia, absence of fingers two to five, and split-foot. It has been described in four males belonging to two generations of the same family. X-linked recessive inheritance is suggested, but autosomal dominant transmission cannot be excluded. Also known as: Van den Berghe-Dequecker syndrome, ulnar hypoplasia-lobster-claw deformity of feet syndrome.