A recessively inherited condition with arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) and a cutaneous phenotype, characterized by peculiar wooly hair and palmoplantar keratoderma. The disease is Naxos disease (MONDO_0011017, a Monarch Disease Ontology entry). Also known as: KWWH type I, NAXOS disease, NXD, keratoderma with woolly hair type I, keratoderma with wooly hair type I, keratosis palmoplantaris with arrythmogenic cardiomyopathy, palmoplantar hyperkeratosis with arrythmogenic cardiomyopathy, palmoplantar keratoderma with arrythmogenic cardiomyopathy.