Monarch Disease Ontology term MONDO_0011451 (cardioencephalomyopathy, fatal infantile, due to cytochrome c oxidase deficiency 1) is any fatal infantile encephalocardiomyopathy in which the cause of the disease is a mutation in the SCO2 gene. Also known as: SCO2 fatal infantile encephalocardiomyopathy, cardioencephalomyopathy, fatal infantile, due to cytochrome C oxidase deficiency type 1, fatal infantile encephalocardiomyopathy caused by mutation in SCO2, mitochondrial complex IV deficiency, nuclear type 2.