An autosomal recessive condition caused by mutation(s) in the MRE11A gene, encoding double-strand break repair protein MRE11. It is characterized by progressive cerebellar degeneration resulting in ataxia and oculomotor apraxia. The disease is MONDO_0011457 (ataxia-telangiectasia-like disorder). Also known as: ATLD, ataxia - telangiectasia-like disorder, ataxia-telangiectasia-like disorder type 1.