Monarch Disease Ontology id MONDO_0011628 (propionic acidemia) is an organic aciduria caused by the deficient activity of the propionyl Coenzyme A carboxylase and is characterized by life threatening episodes of metabolic decompensation, neurological dysfunction and that may be complicated by cardiomyopathy. Also known as: GLYCINEMIA, ketotic, ketotic II glycinemia, ketotic glycinemia, ketotic hyperglycinemia, propionic aciduria, propionyl-CoA carboxylase deficiency.