Carney-Stratakis syndrome is a recently described familial syndrome characterized by gastrointestinal stromal tumors (GIST) and paragangliomas, often at multiple sites. The disease is Carney-Stratakis syndrome (MONDO_0011740). Also known as: Carney dyad, Carney-Stratakis dyad, gist-paraganglioma dyad, paraganglioma and gastric stromal sarcoma.