Monarch Disease Ontology entry MONDO_0011760 (Scheie syndrome) is the mildest form of mucopolysaccharidosis type 1 (MPS1), a rare lysosomal storage disease, characterized by skeletal deformities and a delay in motor development. Also known as: MPS I S, MPS1S, MPSIS, mucopolysaccharidosis type 1S, mucopolysaccharidosis type IS, mucopolysaccharidosis type V.