Monarch Disease Ontology term MONDO_0011812 (Duane-radial ray syndrome) can be described as follows. A syndrome of multiple congenital anomalies and is characterized by ocular manifestations (uni- or bilateral Duane anomaly (95% of cases), congenital optic nerve hypoplasia or optic disk coloboma), bilateral deafness and radial ray malformation that can include thenar hypoplasia and/or hypoplasia or aplasia of the thumbs; hypoplasia or aplasia of the radii; shortening and radial deviation of the forearms; triphalangeal thumbs; and duplication of the thumb (preaxial polydactyly).The phenotype overlaps with other SALL4>/i> related disorders including acro-renal-ocular syndrome and Holt-Oram syndrome (see these terms). Transmission is autosomal dominant. Also known as: DR syndrome, DRRS, Duane anomaly with radial ray abnormalities and deafness, Okihiro syndrome, acro-renal-ocular syndrome, acrorenocular syndrome.