MONDO_0011870 (annular epidermolytic ichthyosis) (AEI) is a rare clinical variant of epidermolytic ichthyosis (EI) characterized by the presence of a blistering phenotype at birth and the development from early infancy of annular polycyclic erythematous scales on the trunk and extremities. Also known as: AEI, ichthyosis, annular epidermolytic.