Monarch Disease Ontology entry MONDO_0012727 (Kawasaki disease) is a rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated. Also known as: Kawasaki syndrome, Kawasaki's disease, MLNS, acute febrile MCLS, acute febrile mucocutaneous lymph node syndrome, acute febrile mucocutaneous lymph node syndrome [MCLS], infantile polyarteritis nodosa, mucocutaneous lymph node syndrome.