Any fatal multiple mitochondrial dysfunctions syndrome in which the cause of the disease is a mutation in the BOLA3 gene. The disease is Monarch Disease Ontology term MONDO_0013675 (multiple mitochondrial dysfunctions syndrome 2). Also known as: BOLA3 deficiency, BOLA3 fatal multiple mitochondrial dysfunctions syndrome, fatal multiple mitochondrial dysfunctions syndrome caused by mutation in BOLA3, multiple mitochondrial dysfunctions syndrome type 2.