Monarch Disease Ontology term MONDO_0013800 (Ehlers-Danlos syndrome, kyphoscoliotic type, 2) is a form of Ehlers-Danlos syndrome, characterized by severe generalized hypotonia at birth with severe early-onset kyphoscolosis along with joint hypermobility (without contractures) leading to recurrent dislocations, and sensorineural hearing impairment. Also known as: EDS with progressive kyphoscoliosis, myopathy, and deafness, EDS with progressive kyphoscoliosis, myopathy, and hearing loss, EDS, kyphoscoliotic and hearing loss type, Ehlers-Danlos syndrome with progressive kyphoscoliosis, myopathy, and deafness, Ehlers-Danlos syndrome with progressive kyphoscoliosis, myopathy, and hearing loss, Ehlers-Danlos syndrome, kyphoscoliotic and deafness type, Ehlers-Danlos syndrome, kyphoscoliotic and hearing loss type.