muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type a, 10 (Monarch Disease Ontology entry MONDO_0014022) is any muscular dystrophy-dystroglycanopathy, type A in which the cause of the disease is a mutation in the RXYLT1 gene. Also known as: RXYLT1 muscular dystrophy-dystroglycanopathy, type A, muscular dystrophy-dystroglycanopathy, type A caused by mutation in RXYLT1.