Monarch Disease Ontology id MONDO_0015612 (Dent disease) is a rare genetic renal tubular disease characterized by manifestations of proximal tubule dysfunction. Also known as: Dent syndrome, Dent's disease, X-linked recessive hypercalciuric hypophosphatemic rickets, X-linked recessive hypophosphatemic rickets, X-linked recessive nephrolithiasis, low-molecular-weight proteinuria with hypercalciuria and nephrocalcinosis, renal Fanconi syndrome with nephrocalcinosis and renal stones.