sporadic infantile bilateral striatal necrosis (MONDO_0016394, a Monarch Disease Ontology identifier) can be described as follows. Sporadic infantile bilateral necrosis is the sporadic form of infantile bilateral striatal necrosis (IBSN), a syndrome of bilateral symmetric spongy degeneration of the caudate nucleaus, putamen and globus pallidus characterized by developmental regression, choreoathetosis and dystonia progressing to spastic quadriparesis. Also known as: ABSN, acute bilateral striatal necrosis, sporadic IBSN, sporadic infantile striatonigral degeneration, sporadic infantile striatonigral necrosis.