progressive sensorineural hearing loss-hypertrophic cardiomyopathy syndrome (Monarch Disease Ontology term MONDO_0016424) can be described as follows. Progressive sensorineural hearing loss - hypertrophic cardiomyopathy is an extremely rare disorder described in one family to date that is characterized by progressive, late onset, autosomal dominant sensorineural hearing loss, QT interval prolongation, and mild cardiac hypertrophy. Also known as: progressive neurosensory deafness-hypertrophic cardiomyopathy syndrome, progressive neurosensory hearing loss-hypertrophic cardiomyopathy syndrome, progressive sensorineural deafness-hypertrophic cardiomyopathy syndrome.