Hermansky-Pudlak syndrome with pulmonary fibrosis (Monarch Disease Ontology term MONDO_0016501) as a complication includes two types (HPS-1 and HPS-4) of Hermansky-Pudlak syndrome (HPS), a multi-system disorder characterized by oculocutaneous albinism, bleeding diathesis and, in some cases, pulmonary fibrosis or granulomatous colitis. Also known as: HPS with pulmonary fibrosis.