heritable pulmonary arterial hypertension (MONDO_0017148) (HPAH) is a form of pulmonary arterial hypertension (PAH), occurring due to mutations in PAH predisposing genes or in a familial context. HPAH is characterized by elevated pulmonary arterial resistance leading to right heart failure. HPAH is progressive and potentially fatal. Also known as: FPAH, HPAH, HpaH, familial pulmonary arterial hypertension, hereditary pulmonary arterial hypertension.