Monarch Disease Ontology term MONDO_0017186 (diazoxide-resistant hyperinsulinism) can be described as follows. Diazoxide-resistant hyperinsulism (DRH) is form of congenital isolated hyperinsulism caused by an abnormal insulin production by B-cells in the pancreas that can be diffuse or focal and is characterized by an excessive/ uncontrolled insulin secretion (inappropriate for the level of glycemia), recurrent episodes of profound hypoglycemia and resistance to medical management with diazoxide. Also known as: diazoxide-resistant hyperinsulinemic hypoglycemia.