steroid dehydrogenase deficiency-dental anomalies syndrome (Monarch Disease Ontology term MONDO_0017904) is an autosomal recessive liver disease which was associated with numerical dental aberrations in a consanguineous Arabi Saudi family. This association suggests that the same gene is involved in both defects. General hypomineralisation and enamel hypoplasia found in this family is thought to be secondary to malabsorption due to liver disease. Also known as: Lyngstadaas syndrome.