Monarch Disease Ontology identifier MONDO_0017935 (hyperinsulinism due to HNF1A deficiency) is a form of diazoxide-sensitive diffuse hyperinsulinism (DHI), characterized by transient or persistent hyperinsulinemic hypoglycemia (HH) in infancy that is responsive to diazoxide, evolving in to maturity-onset diabetes of the young subtype 1 (MODY-1) later in life. Also known as: hyperinsulinemic hypoglycemia due to HNF1A deficiency.