peripheral primitive neuroectodermal tumor (MONDO_0018271) is a small round cell tumor with neural differentiation arising from the soft tissues or bone. Also known as: PPNET, pPNET, peripheral PNET, peripheral neuroectodermal neoplasm, peripheral neuroectodermal tumor, peripheral neuroectodermal tumour, peripheral neuroepithelioma, peripheral primitive neuroectodermal neoplasm.