The autosomal recessive form of distal renal tubular acidosis (dRTA) characterized by hypokalemic hyperchloremic metabolic acidosis. Deafness often occurs either early or later on in life but may be absent or never be diagnosed. The disease is MONDO_0018440 (autosomal recessive distal renal tubular acidosis). Also known as: AR dRTA, autosomal recessive distal RTA, autosomal recessive distal renal tubular acidosis (disease), distal renal tubular acidosis (disease), autosomal recessive.