inborn disorder of branched-chain amino acid metabolism (MONDO_0019242, a Monarch Disease Ontology entry) can be described as follows. An inherited metabolic disease that is has its basis in the disruption of branched-chain amino acid metabolic process. Also known as: disorder of branched-chain amino acid metabolism, inborn branched-chain amino acid metabolic process disorder, inborn error of branched-chain amino acid metabolic process, rare inborn error of branched-chain amino acid metabolic process.