Stargardt disease (Monarch Disease Ontology term MONDO_0019353), also known as Stargardt 1 (STGD1), is an autosomal recessive form of retinal dystrophy that is usually characterized by a progressive loss of central vision associated with irregular macular and perimacular yellow-white fundus flecks, and a so-called ''beaten bronze'' atrophic central macular lesion. Also known as: Stargardt 1, fundus flavimaculatus.