A form of Bartter syndrome characterized by maternal polyhydramnios, premature delivery, salt loss, polyuria and sensorineural deafness, associated with hypokalemic and hypochloremic metabolic alkalosis, increased levels of plasma renin and aldosterone, and low to normal blood pressure. Urinary calcium excretion rates are variable, and nephrocalcinosis is typically absent. The disease is Monarch Disease Ontology entry MONDO_0019524 (Bartter syndrome type 4). Also known as: Bartter syndrome type IV, Bartter syndrome with sensorineural deafness.