aortic valve atresia (MONDO_0019808) is a rare congenital heart defect characterized by the complete failure of the aortic valve to open. It is manifested during infancy with cyanosis, dyspnea, and rapidly progressing heart failure. Also known as: aortic valve atresia (disease), congenital aortic valve atresia, congenital atresia of aortic valve.