progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal dominant 1 (Monarch Disease Ontology term MONDO_0024528) is any autosomal dominant progressive external ophthalmoplegia in which the cause of the disease is a mutation in the POLG gene. Also known as: PEOA1, POLG autosomal dominant progressive external ophthalmoplegia, autosomal dominant progressive external ophthalmoplegia caused by mutation in POLG, progressive external ophthalmoplegia, autosomal dominant 1.